I-Aplasia yezinso

I-apulasia yezinso (uRussell Silver Syndrome) ingenye yezinkinga ezingabonakali zokuthuthukiswa kwezinso. Ibonakala ngokuntuleka okuphelele kwesigungu noma ukuthuthukiswa kwayo. Lesi sifo singashukumisa ukubukeka kwe-pyelonephritis, nephrolithiasis nomfutho wegazi ophezulu.

Izimpawu ze-aplasia yezinso

I-aplasia yezinso ivela lapho umsele we-methanephros ungakhuli ku-metanephrogenic blastema. I-ureter ingaba yinto evamile futhi ifushane. Ezimweni ezingavamile, akusikho ngokuphelele. Isibonakaliso esivame ukwedlula zonke se-aplasia yezinso zesobunxele noma kwesokudla sinciphisa inani lomchamo noma ukungabi khona kwayo. Futhi, ukungabi khona kwengxenye eyodwa yalesi sitho kuvumela i- renlic coal eyodwa (lokhu kuhlaselwa ubuhlungu obunzima obuhambisana ne-anuria). Azikho ezinye izimpawu kule ngozi.

Ukuhlonza izinhlanzi zezinso

Ukuthola i-aplasia yezinso ezinhlangothini kwesobunxele noma kwesokudla, kubalulekile ukwenza ukuhlolwa kwe-ultrasound kwesigxobo esiswini. Futhi, ukuba khona kwe-organ engaphansi kokuthuthukiswa noma ukungabikho kwayo kungathathwa ngokusebenzisa:

44.0-80.0 i-μmol / L iyinhlangano evamile yokudala i-creatinine egazini labesifazane, kodwa nge-aplasia yezinso lesi sibonakaliso singanciphisa kancane. Ngakho-ke, uma kunezibonakaliso ze-pathology enjalo, kufanele futhi uthathe ukuhlolwa kwegazi.

Ukwelashwa kwe-apsosia yezinso

I-aplasia yezinso ezilungile noma kwesokunxele ngokuvamile ayidingi ukwelashwa kwezokwelapha. Ukuze ulondoloze impilo yomuntu esimweni esivamile, udinga kuphela ukulandela ukudla okuhloswe ukunciphisa umthwalo kwizinso zesibili. Uma isiguli sinomfutho wegazi ophakeme, kufanele uthathe izidakamizwa.

Ukuhlinzeka ngokuhlinzeka ngokuhlinzwa nge-aplasia kusetshenziswe kuphela lapho: