I-neuroblastoma ye-retroperitoneal isikhala

I-neuroblastoma yisifo esibi esiyingozi esithinta isistimu yomzwelo ezwelayo. Ngokuvamile, i-tumor ivela ezinganeni kuze kube seminyakeni emibili esikhaleni se-retroperitoneal. Kulokhu, ukuthuthukiswa kwalesi sifo kuqala ngama-gland adrenal. Futhi, i-tumor enkulu ingathinta izicubu eduze komgogodla wengane - esifundeni se-thoracic nesibeletho.

Izimbangela zokubonakala kwe-neuroblastoma

Kuze kube manje, ososayensi abakwazi ukuchaza ngokucacile ukuthi kungani lesi sifo esiyingozi sibonakala. Kuyaziwa ukuthi i-neuroblastoma ivela kuma-embryonic cells, ama-neuroblast. Izimpande zesifo zilele ekuziphatheni nasekuguqulweni kwamaseli. Kwezinye izimo, ukuvuvukala embulus kungatholakala ngesikhathi sokuhamba kwe-ultrasound.

Ziyini izimpawu ze-neuroblastoma ye-retroperitoneal?

Isisu esinonya kakhulu siphuthuma futhi singakhuthuka ngokushesha, okuholela ekubunjweni kwemithi. Nakuba kunezimo lapho ukwelashwa okuzenzekelayo kuvele kungazelelwe ngaphandle kokungenelela kwezokwelapha. Futhi kwezinye iziguli, amangqamuzana abulalayo aguqulwa abe amangqamuzana angama-benign.

I-neuroblastoma ye-retroperitoneal isikhala iholela ekwandeni kwesisu somntwana, ngokuvamile kuvusa ubuhlungu esifundeni sesisu.

Ngokuvamile, lesi sifo siholela ekuzikhukhuleni, ukukhubazeka ukusebenza kwamathumbu nesisu. Ukushisa komzimba nomfutho wegazi kungakhula. Ngaphezu kwalokho, ingane ingakwazi ukulahlekelwa ukudla, ilahlekelwe isisindo ngokushesha.

I-Neuroblastoma Diagnosis

Ukuze ufake ukuxilongwa okufanele nge-neuroblastoma bese uqala ukwelashwa okulungile, kubalulekile ukuthi uhlaziye ngokuphelele. Nge-neuroblastoma, ukuhlolwa kwakhe ngokwemvelo kuyasetshenziswa kabanzi, kokubili isisu ngokwayo kanye ne-metastases.

Okubalulekile ukuqonda isigaba sesifo yi-ultrasound kanye ne-tomography ehlanganisiwe.

Izigaba ezine ze-neuroblastoma ye-retroperitoneal

Ukwelashwa okuqhubekayo kanye nomphumela wayo ngokuqondile kuxhomeke esiteji sesifo. Kuvunyelwe ukuhlukanisa izigaba ezine zesigaba sesi sifo. Kodwa kufanele wazi ukuthi uma lesi sifo siphathwa kahle esigabeni sokuqala noma sesibili, amathuba okunciphisa ayancishiswa kakhulu ezinyathelweni zesithathu nesine. Ake sicabangele ngokuningiliziwe.

  1. І isigaba. Ukukhishwa okungenzeka okungenzeka ukukhishwa kwesakhiwo esibi.
  2. ІІA isigaba. Mhlawumbe ukususwa ngokushesha kwe-neuroblastoma enkulu.
  3. Isigaba se-IIB. I-neuroblastoma ingaba yinye. Kukhona kungenzeka ukuthi ususwe ngokuphelele, noma iningi laso.
  4. Isigaba sigaba. Ngalesi sigaba, i-tumor ingaba yodwa, iphakathi, noma ishaya ohlangothini oluhlukile. Futhi ama-metastase ema-lymph nodes abonakala. Ayikwazi ukulondoloza ezingaphezu kuka-55-60% zezingane.
  5. IV isigaba. Ukuhlukunyezwa okwenziwe kabanzi nge-metastases kuma-lymph nodes, izicubu zethambo nezinye izitho. Esinda ngaphezu kwengxenye yezingane ezigulayo.
  6. IVS isigaba. Kubonakala izimbala ezigabeni zokuqala nezibili, futhi kuthinta nesibindi, isikhumba kanye namathambo esifuba.

I-neuroblastoma yisifo esiyingozi kakhulu. Izindlela eziyinhloko zokwelapha - ukususwa okusheshayo kwemfundo engathandeki, ukwelashwa kwamakhemikhali kanye nokwelashwa kwemisebe.

Kuye ngesigaba sesifo, ukwelashwa okuhlukile kusetshenziswa. Uma lesi sifo sisesigaba sokuqala noma sesibili, njengombuso, ukungenelela kokuhlinzwa nge-chemotherapy esedlule kunqunywe. Isigaba sesithathu sokuthuthukiswa kwesisu singasebenzi, ngakho-ke ingane imisiwe ngamakhemikhali. Esigabeni sesine, inqubo yokuhlinzwa yenziwa ngokulandelwa komuthi we-marrow transplantation. Kubaluleke kakhulu ukubona lesi sifo ngesikhathi. Ekuqaleni izinyathelo zithathwa, zikhuphuka amathuba okubuyiselwa.