I-torsion dystonia yisifo esingavamile lapho umsindo we-muscle uphazamiseka futhi kuphazamiseka ukuphazamiseka kwezimo ezihlukahlukene. I-pathology inemvelaphi yezinzwa kanye nenkambo engapheliyo eqhubekayo. Kuhlotshaniswa nokunqotshwa nokuphazanyiswa komsebenzi wezakhiwo zobuchopho obujulile obhekene nokuhlukunyezwa kwamasipha.
Izinhlobo ze-torsion dystonia
Kuye nge-etiology yesifo, kunezinhlobo ezimbili:
- Idiopathic torsion dystonia - ivela ngenxa yezinto eziphilayo, isb. ifa.
- I-torsion symptytic dystonia - iqala ukuhlukunyezwa okuhlobene nokulimala ezingxenyeni ezithile zobuchopho (isb., I-hepatocerebral dystrophy, izicubu zobuchopho, izifo ezingezansi).
Kuye ngendawo, ukusabalala kwezifo ezibangelwa yi-pathological is:
- I-torsion yendawo yase-dystonia - lesi sifo sithinta amanye amaqembu omzimba (imisipha yentamo, imilenze, izingalo), ivame kakhulu.
- I-torsion Genery dystonia - lesi sifo siphuthuka kancane kancane, okubandakanya inqubo yokwelapha imisipha yangemuva, sonke isiqu, ubuso, kanye nobukhulu bokubonakaliswa kuyaqiniswa.
Izimpawu ze-tory dystonia:
- ukwephulwa kwemali;
- ukunyakaza okuzimele;
- iziqu zemisipha yezinyawo, i-trunk, intamo, ebonakala ngokunyakaza okungajwayelekile okujikelezayo;
- ukukhathazeka kwenkulumo;
- izimpande zemisipha yomhlathi;
- i-spasm yezinkophelo;
- "Bifurcation" wombono, njll.
Ngokuvamile, nge-etiology yokuzalwa, ukubonakaliswa kokuqala kwalesi sifo kubonakala kuneminyaka engu-15-20. Okokuqala, ukuphazamiseka nokuphazamiseka kwenzeka uma uzama ukuhamba, ngokucindezeleka ngokomzimba noma ngokomzwelo. Kamuva izimpawu ziqala ukuzibonakalisa esimweni sokuphumula.
Ukwelashwa kwe-torsion dystonia
Ezimweni eziningi, amaqembu alandelayo adakamizwa anikezwe ukwelashwa kwesifo:
- imisipha yokuphumula ;
- i-adrenoblockers;
- amalungiselelo okucholinolytic;
- i-glucocorticoids ;
- antipsychotics;
- izidakamizwa.
Futhi kungabekwa imizimba yokwelashwa, ukusikhipha umzimba, ukwelashwa kwe-physiotherapy. Ukusebenza kangcono ukwelapha okuhlinzekwa kwe-torsion dystonia, lapho kusetshenzwa khona izinzwa zomzimba noma ngokubhujiswa kwezinhlaka ezingaphansi kwebuchopho. Ukungenelela kokuhlinzeka kungaphumelela imiphumela emihle kuma-80% wamacala.