Isifo se-anemia yesifo yisifo sokufa esithinta uhlelo lwe-hematopoietic. Kuyisici lapho kudalwa khona uhlaka olujwayelekile lwe-hemoglobin. Lokhu kuveza isakhi esingavamile eshintsha isakhiwo samangqamuzana egazi abomvu - ahlala isikhathi eside (afana nesigqoko, yingakho igama lihamba).
Izimpawu ze-anemia ye-sickle-cell
Kubantu, lesi sifo sidonsa i-anemia yesisindo yisimiso sesici. Ngokuvamile zonke izimpawu zesikhonzi zibangelwa yi-thrombosis noma i-anemia. Kunezibonakaliso eziyisisekelo ezinjalo:
- isikhumba sithatha i-tint ephuzi;
- i-hypoxic syndrome;
- le skeleton likhubazekile;
- izinkinga nezitho zangaphakathi.
Kubalulekile ukuqaphela ukuthi i-sickle cell-anemia ibangelwa ukubukeka kwe-thrombi. Kulesi simo, ukuvuvukala ezingxenyeni ezahlukene zezitsha kungase kwenzeke, okuhambisana nokuzwa okubuhlungu.
Zonke izimpawu zihlukaniswe ngokomzimba ngamaqembu amabili - lokhu kuxhomeke ezimbangela eziyinhloko zokugula:
- ngenxa ye- thrombi ohlelweni lokujikeleza;
- ngenxa yokubhujiswa ngokweqile kwamangqamuzana egazi abomvu.
Ukuxilongwa kwe-sickle cell anemia
Ukuxilongwa nokuphathwa kwalesi sifo kusebenzelana nodokotela-isifo semfuyo. Kungenakwenzeka ukusekela ngokunembile isigaba sesifo, ukuthembela kuphela ekubonakalweni kwangaphandle. Iqiniso liwukuthi izimpawu ezifanayo zenzeka ezifweni eziningi zegazi. Ukuze kutholakale ukuxilongwa okugcwele, okulandelayo kusetshenziselwa:
- ukuhlolwa kwegazi jikelele kanye negazi ;
- I-Ultrasound yezingxenye zomzimba ngamunye;
- I-X-ray;
- i-electrophoresis ye-hemoglobin.
Ukwelapha i-sickle cell anemia
Okwamanje, lesi sifo sibhekwa singelapheki. Ngesikhathi esifanayo ukuvimbela ukukhula kwesifo kubalulekile ukuhola indlela yokuphila enempilo. Ngakho-ke, isibonelo, abantu abahlukunyezwa yi-sickle-cell anemia bayagula kancane uma bedla ukudla okunempilo, bangaphuzi, bangabhemi, benza izivivinyo. Lokhu kuthuthukisa isimo jikelele.