I-Myasthenia gravis - izimpawu, izimbangela

Esinye sezifo ezidumile kakhulu ezizimele ngokuzenzakalelayo i-myasthenia gravis. Lesi sifo sithinta uhlelo lwe-neuromuscular. Izimbangela ze-myasthenia gravis zingase zihluke, kodwa izimpawu zesifo sezinto eziningi eziphilayo zifanayo. Lesi sifo sibhekene nokukhathala okwandayo emafayilini omzimba. I-Myasthenia gravis, bobabili besilisa nabesifazane, kodwa njengoba isipiliyoni sibonisa, ubulili obuhle besifo buvame kakhulu.

Izimbangela ze-myasthenia gravis

Naphezu kokuthi ukuhlolwa kwesifo sekuqhubeka iminyaka eminingi, ngokuqinisekile ukuthi i-myasthenia gravis iyaqala, ochwepheshe abakwazi ukusho. Ngokusobala, ukugujwa kwesintu kudla indima enkulu ekuthuthukiseni lesi sifo. Kungenxa yalesi sizathu ukuthi i-myasthenia gravis ngezinye izikhathi ingabonwa ngisho nasezinsana. Nokho, ngemuva kwamasonto ambalwa, ngisho nezinsuku, ukugula kwezingane kudlula ngokwabo.

Enye imbangela engenzeka ye-myasthenia gravis iyisisu se-thymus noma i- thymus gland . Kulokhu, ama-antibodies atholakale ezicukwaneni zelungu elilimaza imitholampilo enempilo ehlanganyela ekuqhekekeni kwemisipha yomzimba. Ama-antibodies anjalo akhiwa ngenxa yokuphazamiseka okwenzeka emajeni we-protini. Isizathu salokhu lokhu isimo esinganelisi samasosha omzimba.

Izimpawu ze-myasthenia gravis

Kunezinhlobo ezintathu eziyinhloko ze-myasthenia gravis:

Zonke zingaba zitholakale noma zitholakale futhi ziholele ekuphumuzeni kwemisipha eminyene. Lokhu kwenzeka ezimweni eziningi ngemuva kokusebenza ngokomzimba.

Uphawu oluyinhloko lwe-myasthenia gravis lumbono ophindwe kabili. Ngokufana nalokhu kubonakaliswa kwesifo, ukushiyeka okungenakuzikhethela kwamajwabu amehlo kungenzeka. Amehlo isiguli asheshe akhathele kunokujwayelekile, futhi lokhu kubonakala ngokumelene nesizinda semithwalo elula ngokwanele.

Ezimweni eziningi, okokuqala, imisipha ihlupheka, izimpendulo ezondliwa ngokuqondile emithanjeni ye-cranial. Esikhathini esizayo, njengoba ukuthuthukiswa kwesifo kungathinta imisipha yentamo, izitho.

Uma isikhathi eside i-myasthenia gravis ihlala ngaphandle kokunakekelwa, izimpawu zesifo sifana. Isibonakaliso esivamile saleso sifo nakho ukwephulwa kwesichazamazwi. Iziguli eziningi emva kokuzikhandla ngokomzimba zibhekene nobunzima, zizama ukuzwakala amagama namazwi alula.

Ngaphezu kwalokho, i-mysthenia gravis, i-bulbar kanye ne-ocular eye gravis gravis ingabonakala ngezimpawu ezilandelayo:

Ku-myasthenia ye-bulbar, phakathi kwezinye izinto, kunezinguquko enkulumweni. Izwi lesiguli liba likhulu, liqhakazile, likhukhumele futhi lilithule. Ifomu elijwayelekile lesi sifo ihambisana nobuthakathaka bemikhawulo. Ekuseni, isimo sesiguli singacatshangwa njengokwanelisayo, kodwa kusihlwa kusihlahloka kancane.

Esikhathini sokuqala emva kokuphumula okufutshane, isimo sesiguli sibuyele emuva evamile. Kodwa ngokuhamba kwesikhathi, izimpawu ze-myasthenia gravis zizohlala ngisho nangemva kokuphumula okugcwele.

Ukubhekana nalesi sifo kungaba nemithi, ehlanganisa i-acetylcholine. Izindlela ezingcono kakhulu ziyi-Proserin noma i-Kalimin. Ukwengeza, i-corticosteroids ne-cytostatics ingabekwa. Uma kunesidingo, isiguli sisuswe i-thymus gland.