Umzimba onempilo uvikelwe ngamasosha omzimba omzimba avela ekuhlaselweni kwegciwane, i-fungal kanye ne-baktheriya, izifo nezinye izici ezingathandeki. I-immunodeficiency eyinhloko iyanqanda umuntu wale nkinga kusukela eminyakeni yokuqala yokuphila, kodwa ingazibonakalisa ekukhuleni. Lesi sifo sidinga ukuqapha okuqhubekayo ngososayensi kanye nokwelashwa eside kakhulu.
Ukuhlukaniswa kwama-immunodeficiencies okuqala okuzalwa
Ukukhubazeka okucatshangelwayo kunezinhlobo ezingu-5, ezibangelwa ukungasebenzi:
1. Ukungakwazi ukuzivikela komzimba:
- i-oroticide;
- isifo sikaDi Georgi;
- i-fermentopathy exhomekeke ku-biotin;
- ukungakwazi ukusebenza kwe-purinucleoside phosphorylase.
2. I-Phagocytic primary immunodeficiency:
- isifo esingenasifo esibuhlungu;
- i-cyclic ne-chronic acyclic neutropenia;
- I-Miller's syndrome ("ama-leukocyte avila".
3. Ukungasebenzi kwamangqamuzana e-humoral:
- ukuqala kwe-immune ekuqaleni;
- I-syndrome kaBruton;
- ukwehluleka kokukhetha ama-immunoglobulins.
4. Ukuntuleka okuhlanganisiwe kwesandulela ngculazi nesisindo:
- I-Wiskott-Aldrich syndrome;
- i-hypocalcemia ;
- i-dysgenisis reticular;
- i-Glanzmann-Riniker syndrome.
Ukuhluleka okuphelele:
- I-edema ka-Quincke-Osler;
- i-lupus erythematosus;
- i-arthritis ye-rheumatoid.
Izimpawu ze-immunodeficiency primary
Azikho izibonakaliso zezici ezivumela ukudalula ngokunembile ukuhlushwa kwezakhi zofuzo. Ukubonakaliswa kwemitholampilo kuyahluka kakhulu kuye ngokuthi uhlobo, ukuma nokuqina kwesifo.
Ukusola ukuthi i-immunodeficiency eyinhloko ingenzeka ngezibonakaliso ezinjalo:
- ukutholakala nezifo ezithathelwanayo nezifo ezithathelwanayo;
- umphumela omncane wokuthatha ama-antibiotics;
- i-candidiasis yesikhumba ne-relapses;
- amaqebelengwane aphuthumayo;
- i-pneumonia 2 nezikhathi eziningi ngonyaka;
- i-otitis engunaphakade, i-sinusitis, i-bronchitis.
Ukwelashwa kwe-primary immunodeficiency
Ukwelashwa kunzima, ngoba awukwazi ukwelapha ukugula. Ukuthuthukisa ikhwalithi yokuphila kweziguli, ukwelashwa okuqhubekayo okungahambisani nomzimba kanye nama-immunoglobulin kuyadingeka, kanye nokukhethwa ngokucophelela kwama-antibacterial, antiviral and antimycotic agents for infections.
Ukwelashwa okunamandla kwezifo ezichazwe kuqukethe ukufakelwa komnkantsha wamathambo, okungcono okwenziwa ngesikhathi esencane. Kodwa kufanele kuqaphele ukuthi lo msebenzi ubiza kakhulu, futhi ngezinye izikhathi kunzima ukuthola umnikezeli ngokuhambisana okwanele.