I-myopathy yisifo lapho ukuphela kweziphetho zezinzwa kubangela ukuba imicu ye-muscle ihlaziye, futhi kuvele i-atrophy emisipha. Kuze kube yamuva, kwakucatshangwa ukuthi isifo esinjalo, njenge-myopathy, sifa kuphela. Kodwa-ke, kubonakala ukuthi ukulimala kanye nokutheleleka, ukungabi namavithamini, izinqubo zokuvuvukala nakho kungabangela ukuthuthukiswa kwe-muscular dystrophy.
Izimpawu zokwehluleka
Ukuthuthukiswa kwalesi sifo kuqala esemncane. Noma kunjalo, ngezizathu ezingezona izakhi zofuzo zokwenzeka kwe-myopathy, ukuthuthukiswa kwayo kungase kwenzeke nangesikhathi esivuthiwe.
Isiguli sinesibindi futhi sinesifo esithile endaweni ethile. Ngokuya ngohlobo lwesifo, ikakhulukazi imisipha yebhande lesigxathu kanye nekhanda, kanye nezitho zomzimba, ziyathinteka. Ukuthuthukiswa kwe-atrophy kwenzeka ngokulinganayo. Ngokumelene nalesi sizinda, amanye amaqembu e-muscle angakhuphuka ngokweqile ngenxa yamathambo namaxhunu asebenzayo. Imisipha enwetshiwe inesisindo esikhulu.
Ngakho-ke, iyini intukuthelo enjalo, futhi yiziphi izinhlobo zezifo ezitholakele kaningi, sizoqonda kabanzi.
Kuncike ekuguqulweni kwezakhi zofuzo eziningana zezifo ezithintekile, kanti iminyaka yesiguli, ukukhubazeka kuhlukaniswe ngezindlela eziningana.
Izinhlobo zokwehluleka
Ifomu le-Erb leJaji
Uhlobo lwe-Erb's myopathy luzobonakala lusondelene neyeshumi leminyaka futhi luyathinta imisipha ye-pelvic, bese iphakamisa ebhande lehlombe. Ngokuvame ukuphawula i-hyperlordosis - ukuvinjelwa komgogodla phambili ngenxa ye-atrophy ye-muscle ngemuva nangesisu. Imisipha emihle yomlomo iphukile, izindebe ziphuma ngaphandle, isiguli asikwazi ukumomotheka. Ukuguqulwa kwezinto kuyashintsha.
I-myopathy kaBeker
I-benecker's benign hypertrophic myopathy ithinta imisipha emilenze yemilenze. Ukuqala kwalesi sifo kuyaqhubeka kancane kancane ngokunyuka okubonakalayo emisipha ye-gastrocnemius nokusabalalisa okuqhubekayo kwe-atrophy kuya eqenjini lezinyosi ze-hip.
Isikhathi esithile isiguli sinethuba lokunyakaza okuzimele. Ukuzamazama kukaBikker, ukwehluleka kwenhliziyo kuyisici.
Myopathy Landuzi-Dezherina
Ukubonakaliswa kwalesi sifo kuqala ebusheni futhi kubonakala nge-atrophy yemisipha yobuso ebusweni. Kulesi simo, isiguli sinezindebe, amajwabu amehlo awawa, kanti ubuso bungabonakali.
I-Atrophy ifinyelela kumisipha yebhande elisehlombe, kepha amandla omsebenzi agcinwa isikhathi eside.
I-Myopathy iso
Ukwehliswa kweso kuyancipha kancane kancane ekuhambeni kwezilwane zamehlo ngokulondoloza okugcwele noma okuyingxenye yombono, futhi ngezinye izikhathi ukubhujiswa kwe-pigmentation ye-retina kukhona. Iyini ukuzamazama kwamehlo akuvezile ngokushesha, ngokungafanele bakholelwa ukuthi izimpawu ezinjalo ziyisici se-primary lesion sama-apula oculomotor.
Kunezinhlobo ezimbili ze-pathology:
- ukucabangela komuntu;
- oculo-farengesal.
Esimweni sesibili, imisipha ye-pharynx iyathinteka.
Ukumangaza okuvuthayo
Uma ukutheleleka komzimba ngezinhlobo ezithile zamabhaktheriya nokuvuvukala emisipha yamathambo, kunomsocoko, obonakala ubuthakathaka emzimbeni, ubuhlungu emathisini, ukuvuvukala nokwenyuka komsebenzi. Lolu hlobo lwesifo lungaphathwa nge-glucocorticosteids.
Kunezinhlobo ezehlukene zokwehluleka ukuvuvukala:
- i-polymyositis;
- dermatomyosis;
- i-polymyalgia ye-rheumatic;
- i-myositis ye- eyeball.
Ukwelashwa kwe-myopathy
Ngokuvamile, ukwelashwa kuyingozi, okuhloswe ngayo:
- Ukubuyiselwa kwezinqubo ze-metabolic kumaseli;
- ukwelashwa kwe-neurology;
- ngcono ukuqhutshwa kwe-neuromuscular.
Faka isicelo se-physiotherapy, ukubhukuda ukuvocavoca. Umphumela omuhle ukusetshenziswa kwezidakamizwa ze-anabolic hormonal, i-ATP.
Zonke izinqubo zenziwa ukunciphisa isimo sesiguli nokunciphisa inqubo yokuchitheka kwemisipha, kodwa ayikwazi futhi ayithinti inkinga yesifo.