I-Myopathy - iyini?

I-myopathy yisifo lapho ukuphela kweziphetho zezinzwa kubangela ukuba imicu ye-muscle ihlaziye, futhi kuvele i-atrophy emisipha. Kuze kube yamuva, kwakucatshangwa ukuthi isifo esinjalo, njenge-myopathy, sifa kuphela. Kodwa-ke, kubonakala ukuthi ukulimala kanye nokutheleleka, ukungabi namavithamini, izinqubo zokuvuvukala nakho kungabangela ukuthuthukiswa kwe-muscular dystrophy.

Izimpawu zokwehluleka

Ukuthuthukiswa kwalesi sifo kuqala esemncane. Noma kunjalo, ngezizathu ezingezona izakhi zofuzo zokwenzeka kwe-myopathy, ukuthuthukiswa kwayo kungase kwenzeke nangesikhathi esivuthiwe.

Isiguli sinesibindi futhi sinesifo esithile endaweni ethile. Ngokuya ngohlobo lwesifo, ikakhulukazi imisipha yebhande lesigxathu kanye nekhanda, kanye nezitho zomzimba, ziyathinteka. Ukuthuthukiswa kwe-atrophy kwenzeka ngokulinganayo. Ngokumelene nalesi sizinda, amanye amaqembu e-muscle angakhuphuka ngokweqile ngenxa yamathambo namaxhunu asebenzayo. Imisipha enwetshiwe inesisindo esikhulu.

Ngakho-ke, iyini intukuthelo enjalo, futhi yiziphi izinhlobo zezifo ezitholakele kaningi, sizoqonda kabanzi.

Kuncike ekuguqulweni kwezakhi zofuzo eziningana zezifo ezithintekile, kanti iminyaka yesiguli, ukukhubazeka kuhlukaniswe ngezindlela eziningana.

Izinhlobo zokwehluleka

Ifomu le-Erb leJaji

Uhlobo lwe-Erb's myopathy luzobonakala lusondelene neyeshumi leminyaka futhi luyathinta imisipha ye-pelvic, bese iphakamisa ebhande lehlombe. Ngokuvame ukuphawula i-hyperlordosis - ukuvinjelwa komgogodla phambili ngenxa ye-atrophy ye-muscle ngemuva nangesisu. Imisipha emihle yomlomo iphukile, izindebe ziphuma ngaphandle, isiguli asikwazi ukumomotheka. Ukuguqulwa kwezinto kuyashintsha.

I-myopathy kaBeker

I-benecker's benign hypertrophic myopathy ithinta imisipha emilenze yemilenze. Ukuqala kwalesi sifo kuyaqhubeka kancane kancane ngokunyuka okubonakalayo emisipha ye-gastrocnemius nokusabalalisa okuqhubekayo kwe-atrophy kuya eqenjini lezinyosi ze-hip.

Isikhathi esithile isiguli sinethuba lokunyakaza okuzimele. Ukuzamazama kukaBikker, ukwehluleka kwenhliziyo kuyisici.

Myopathy Landuzi-Dezherina

Ukubonakaliswa kwalesi sifo kuqala ebusheni futhi kubonakala nge-atrophy yemisipha yobuso ebusweni. Kulesi simo, isiguli sinezindebe, amajwabu amehlo awawa, kanti ubuso bungabonakali.

I-Atrophy ifinyelela kumisipha yebhande elisehlombe, kepha amandla omsebenzi agcinwa isikhathi eside.

I-Myopathy iso

Ukwehliswa kweso kuyancipha kancane kancane ekuhambeni kwezilwane zamehlo ngokulondoloza okugcwele noma okuyingxenye yombono, futhi ngezinye izikhathi ukubhujiswa kwe-pigmentation ye-retina kukhona. Iyini ukuzamazama kwamehlo akuvezile ngokushesha, ngokungafanele bakholelwa ukuthi izimpawu ezinjalo ziyisici se-primary lesion sama-apula oculomotor.

Kunezinhlobo ezimbili ze-pathology:

Esimweni sesibili, imisipha ye-pharynx iyathinteka.

Ukumangaza okuvuthayo

Uma ukutheleleka komzimba ngezinhlobo ezithile zamabhaktheriya nokuvuvukala emisipha yamathambo, kunomsocoko, obonakala ubuthakathaka emzimbeni, ubuhlungu emathisini, ukuvuvukala nokwenyuka komsebenzi. Lolu hlobo lwesifo lungaphathwa nge-glucocorticosteids.

Kunezinhlobo ezehlukene zokwehluleka ukuvuvukala:

Ukwelashwa kwe-myopathy

Ngokuvamile, ukwelashwa kuyingozi, okuhloswe ngayo:

Faka isicelo se-physiotherapy, ukubhukuda ukuvocavoca. Umphumela omuhle ukusetshenziswa kwezidakamizwa ze-anabolic hormonal, i-ATP.

Zonke izinqubo zenziwa ukunciphisa isimo sesiguli nokunciphisa inqubo yokuchitheka kwemisipha, kodwa ayikwazi futhi ayithinti inkinga yesifo.