I-Gilbert syndrome iyisifo esiyinzalo esithinta isici sofuzo esihilelekile ekudambiseni umzimba kwe- bilirubin . Ngenxa yalokho, inani lempahla egazini liyakhula, futhi ngesinye isikhathi isiguli sinomzimba omncane we-jaundice - okungukuthi, isikhumba kanye nama-mucous aphuzi. Ngesikhathi esifanayo, zonke ezinye izilinganiso zegazi kanye nezivivinyo zesibindi zihlala zijwayelekile.
I-Gilbert's syndrome - yini ngamazwi alula?
Isizathu esiyinhloko saleso sifo ukuphikisana kwegeneli elibhekene ne-glucuronyl transferase, i-enzyme ye-hepatic eyenza ukushintshaniswa kwe-bilirubin kungenzeka. Uma le enzyme emzimbeni enganele, le nto ayinakudliwa ngokuphelele, futhi iningi layo lingene egazini. Lapho ukuhlushwa kwe-bilirubin kwanda, i-jaundice iqala. Ngamanye amazwi, ukumane ukhulume: Isifo sikaGilbert yisingakwazi isibindi ukuphuza imithi enobuthi ngobuningi obanele futhi isuse.
I-Gilbert's syndrome - izimpawu
Lesi sifo kaningi kaningi izikhathi ezingu-2-3 kaningi okutholakala kumadoda. Njengomthetho, izimpawu zokuqala zalo zivela eminyakeni engu-3 ukuya kweyishumi nambili. I-Gilbert syndrome ingane ingathola "ngefa" kubazali. Ngaphezu kwalokho, lesi sifo sibhekene nesimo sangemva kwesidlala eside, izifo, ukucindezeleka ngokomzimba nangokomzwelo. Ngezinye izikhathi lesi sifo sibonakala ngenxa yokudla kwamahomoni noma izinto ezifana ne-caffeine, salicylate ye-sodium, i-paracetamol.
Isibonakaliso esikhulu se-syndrome yi- jaundice . Kungaba okuphakathi (kubonakala ngemva kokuphuza utshwala, ngenxa yokudlulela ngokomzimba noma ukulimala kwengqondo) futhi okungapheli. Kwezinye iziguli, izinga le-bilirubin e-Gilbert's syndrome likhuphuka kancane, futhi isikhumba sitholakale nje sithokozela kancane, kuyilapho kwabanye ngisho nalabo abamhlophe bamehlo baba yi-ocher bright. Ezimweni ezingavamile, i-jaundice iba nebala.
Ngaphandle kokuphuzika kwesikhumba kanye nezinambuzane ezimangcwaba, isifo sikaGilbert sinempawu ezilandelayo:
- ukulala;
- ubuthakathaka;
- ukukhathala okusheshayo;
- i-heartburn ;
- ukubukeka komunwe omunyu emlonyeni;
- ukuwohloka kwesifiso;
- ukuvula;
- uzizwa unesizungu ku-hypochondrium efanele;
- isifo se-stool (iziguli zivame ukukhononda ngesifo sohudo ehambisana nokuqothulwa);
- Ukwandiswa kwesibindi (kwenzeka kuphela kuma-25% wamacala, kanti ubukhulu bomzimba buyashintsha kancane, futhi ukugqama kuhlala kungenabuhlungu).
I-Gilbert's syndrome - ukuxilongwa
Ukuze unqume lesi sifo, udinga ukuqhuba izifundo eziningana zomtholampilo ngesikhathi esisodwa. Ukuhlolwa kwegazi okudingekayo kwe-Zibera syndrome. Ngaphezu kwalokho, isiguli sinikezwa:
- ukuguqulwa kwamanzi;
- isifundo sokuhlushwa kwe-bilirubin egazini;
- amasampula we-bilirubin (nge-nicotinic acid, indlala noma phenobarbital);
- I-Ultrasound yesigxobo sesisu ;
- ukuhlaziywa kwamathambo we-sterbilin;
- ihlaziya nge-alkaline phosphatase, i-GGTP, i-AsAT, i-ALT.
Ukuhlaziywa kwe-Gilbert's syndrome - okulotshiwe
Imiphumela yezinhlolovo ze-laboratory ihlale ilukhuni ukuhlukana. Ngokuyinhloko, uma kuningi kakhulu kubo, njengokuthola lesi sifo. Uma kukhona ukusola kwe-Zhibera syndrome, futhi i-bilirubin ekuhlaleni idlula imikhuba ka-8.5 - 20.5 mmol / l, kanti ukuxilongwa kuqinisekisiwe. Isibonakaliso esingahle siwukuba khona kwezinto ezinobuthi emcinini. Okubalulekile - izimpawu ze-hepatitis ye-viral ku-syndrome azitholakali.
Ukuhlaziywa kwamaGenesis kaGilbert's syndrome
Ngenxa yokuthi lesi sifo sivame ukuzalwa, imisebenzi yokuxilongwa ezimweni eziningi ihlanganisa ucwaningo lwe-DNA. Kukholelwa ukuthi lesi sifo sidluliselwa emntwaneni kuphela uma abazali bobabili bephethe izakhi zofuzo ezingavamile. Uma esinye sezihlobo singenalo, umntwana uzozalwa enempilo, kodwa ngesikhathi esifanayo uyoba umphathi wegciwane "elingalungile".
Thola ukuthi i-homozygous Gilbert syndrome e-DNA ukuxilongwa kungaba ngokuhlola inombolo ye-TA iphinda. Uma bekhona esifundeni sesiphakamiso segesi 7 noma ngaphezulu, ukuxilongwa kuqinisekisiwe. Ochwepheshe bancoma ngokuqinile ukuthi bahlole ukuhlolwa kokubeletha ngaphambi kokuqala ukwelashwa, ikakhulu lapho ukwelashwa ngezidakamizwa ezinemiphumela ye-hepatotoxic kulindeleke.
Indlela yokuphatha ngayo i-Gilbert's syndrome?
Kubalulekile ukuqonda ukuthi lesi akusona isifo esijwayelekile. Ngakho-ke, ekwelapheni okukhethekile uGilbert's syndrome ayidingi. Ngemva kokufunda ngokuxilongwa kwabo, iziguli zinconywa ukuba zibukeze ukudla - ukunciphisa ukusetshenziswa kosawoti, okunamandla, - ukuzama ukuzivikela ekucindezelekeni nasekuhlangenwe nakho, ukuyeka imikhuba emibi, uma kungenzeka ukuba usebenzise indlela yokuphila enempilo. Kalula nje, ayikho imfihlo yokwelapha i-Gilbert's syndrome. Kodwa zonke izinyathelo ezichazwe ngenhla zingaletha izinga le-bilirubin elijwayelekile.
Izidakamizwa nge-Gilbert's syndrome
Ukuqokwa noma imuphi umuthi kufanele ube ngumchwepheshe. Njengomthetho, izidakamizwa ngeGilbert syndrome zisetshenziswa kanje:
- Imithi evela eqenjini le-barbiturate. Lezi zidakamizwa zinomthelela we-antiepileptic, ngokufana nokunciphisa izinga le-bilirubin.
- I-hepatoprotectors . Vikela isibindi emiphumeleni emibi ye-stimuli.
- Ngaphambi kokuphazamiseka kwe-dyspeptic, i-Gilbert's syndrome iphathwa nge-antiemetics kanye ne-enzymes yokugaya ukudla.
- Ukungena okufake isandla kufaka isandla ekususweni okusheshayo kwe-bilirubin kusuka emathunjini.
Ukudla ku-Gilbert's syndrome
Eqinisweni, ukudla okunempilo kuyisihluthulelo sokubuyiselwa okuphumelelayo kwezinga elijwayelekile le-bilirubin egazini. Ukudla nesifo sikaGilbert kuyadingeka. Kodwa kuyasebenza. Iziguli ezitholakalayo lokhu zivunyelwe ukudla:
- isinkwa sikakolweni;
- i-fat cottage shizi encane;
- inyama yenkomo ephansi;
- inkukhu ebilisiwe;
- isobho kwi-bulbone yemifino;
- i-porridge encane;
- izithelo (kodwa hhayi acidic);
- i-compotes;
- itiye elibuthakathaka.
Futhi imikhiqizo ngeGilbert's disease inqatshelwe kanje:
- i-fresh baked bakery;
- i-pepper;
- i-ayisikhilimu;
- inyama enenhlanzi nenhlanzi;
- isipinashi;
- isinqumelo;
- i-sorrel;
- isinaphi;
- utshwala;
- ikhofi yemvelo.
I-Gilbert syndrome - ukwelashwa ngamakhambi abantu
Akunakwenzeka ukuthembela kuphela kwezinye izindlela zokwelapha. Kodwa isifo sika-Augustin Gilbert singesinye sezifo ezinjalo, lapho ukwelashwa kwabantu kuyamukelwa ngisho nongcweti abaningi. Into eyinhloko ukuxoxa uhlu lwemithi nodokotela ozofika, uzibeke ngokucacile umthamo wakho futhi ungakhohlwa ukuthatha zonke izivivinyo zokulawula ezidingekayo.
Gilbert syndrome - ukwelashwa kwamafutha ngoviniga noju
Izithako:
- amafutha omnqumo - 0,5 l;
- I-honey honey - 0,5 kg;
- i-apula cider uviniga - 75 ml.
Ukulungiselela, sebenzisa:
- Hlanganisa zonke izithako kahle esitsheni esisodwa bese uthele ingilazi, isitsha esivaliwe kahle.
- Gcina umuthi endaweni emnyama ebomvu (egcekeni elingaphansi leqrijini, isibonelo).
- Ngaphambi kokusetshenziswa, amanzi kufanele avinjelwe yi-spoon enkuni.
- Phuza cishe 15 - 20 ml imizuzu engu-20 kuya ku-30 ngaphambi kokudla izikhathi ezintathu kuya kweziyisihlanu ngosuku.
- I-jaundice izoqala ukwehla ngosuku lwesithathu, kodwa isidakamizwa kufanele sidakwe okungenani ngesonto. Ukuphuka phakathi kwezifundo kumele kube okungenani amasonto amathathu.
Ukwelashwa kwe-Gilbert's syndrome nge-burdock
Izithako:
- amaqabunga e-burdock;
- amanzi - 2 tsp.
Ukulungiselela, sebenzisa:
- Kunconywa ukusebenzisa amaqabunga amasha aqoqwe ngoMeyi, lapho aqukethe inani eliphelele lemisebenzi ewusizo.
- Sula imifino ngamanzi.
- Umconywa unconywa ukuphuza ama-15 ml kathathu ngosuku izinsuku ezingu-10.
Yini eyingozi eGilbert syndrome?
Lesi sifo asiholeli ekufeni futhi izinga lokuphila alibi kakhulu. Kodwa kulokhu, i-Gilbert's syndrome inemiphumela emibi ngemva kwakho konke. Phakathi neminyaka, ezinye iziguli ezine-jaundice zingahlakulela ukukhathazeka kwengqondo. Yini engabangela kakhulu inqubo yokuzivumelanisa nomphakathi futhi iphoqele umuntu ukuba aye kumuntu ongokwengqondo.
Ezimweni ezingavamile, i-Gilbert syndrome ikhiqiza amatshe aqoshiwe e-bile noma emidayeni yesisu. Uma kwenzeka lokhu, ngenxa yokuqoqwa kwemali eqondile ye-bilirubin engaqondakali, ukugwinya. Izinguquko zesibindi cishe azikhathazi. Kodwa uma ungazitholi utshwala, ukudla okulimazayo futhi uthathe imithi engalawuleki, isifo sofuba singakhula.
I-Gilbert's syndrome nokukhulelwa
Ngaso leso sikhathi kuyadingeka ukuzolalisa bonke omama esikhathini esizayo: lesi sifo nokukhulelwa akubandakanyi nomunye. I-Gilbert's syndrome ayifaki ingozi kumfazi noma ingane yakhe yesikhathi esizayo. Ingozi enkulu yokuveza isifo ngesikhathi esithakazelisayo kungenakwenzeka ukuthatha leyo mithi ejwayele ukusetshenziselwa ukunciphisa isimo seziguli.
I-Gilbert syndrome izuzwe njengefa, kodwa umama ozayo anganciphisa inani le-bilirubin egazini. Ngalokhu udinga:
- Ukuqeda ngokuphelele umsebenzi wokuzivocavoca.
- Yeka utshwala.
- Gwema ngisho nokucindezeleka okuncane.
- Ungalali nhlobo.
- Hlala elangeni isikhathi esilinganiselwe.