I-Kawasaki syndrome ibizwa ngokuthi isifo esibucayi se-systemic, esibhekene nokulimala okukhulu kwesitshalo segazi esikhulu, esiphakathi nesincane, okuhambisana nokudilizwa kwezindonga zamasongo kanye nokubunjwa kwe-thromboses. Lesi sifo sasiqale sichazwa eminyakeni yama-60. ikhulu lokugcina eJapane. Isifo se-Kawasaki senziwa ezinganeni ezineminyaka engu-2 ubudala kuze kube ngu-8, futhi kubafana cishe kabili kaningi njengamantombazane. Ngeshwa, imbangela yokubonakala kwalesi simo ayisaziwa.
I-Kawasaki syndrome: izimpawu
Njengomthetho, lesi sifo sibonakala ngokuqala kanzima:
- ukwanda kwamazinga okushisa angekho ngaphansi kuka-38.5 ° C;
- ukuboshwa komphimbo, ulimi, izindebe ezomile, izintende zezandla nezinyawo;
- ukwanda kwenzalo ye-lymph nervous.
Bese ubonakala ukuqhuma kwe-macular kombala obomvu ebusweni, i-trunk, izingqikithi zomntwana. I-diarrhea ne-conjunctivitis kungenzeka. Ngemva kwamasonto angu-2-3, futhi kwezinye izimo ngisho nangesikhathi eside, zonke izimpawu ezichazwe ngenhla ziyanyamalala, futhi umphumela omuhle uyenzeka. Noma kunjalo, i-Kawasaki syndrome ezinganeni ingaholela ezinkingeni: ukuthuthukiswa kwe-infarction ye-myocardial, ukuhlukana komshini we-coronary. Ngeshwa, ukufa okungu-2% kwenzeka.
Isifo se-Kawasaki: ukwelashwa
Lapho ukwelashwa kwesifo, ukwelashwa kwama-antibacterial akusebenzi. Ngokuyinhloko, inqubo isetshenziselwa ukugwema ukwandiswa kwemithambo ye-coronary yokunciphisa ukulimala. Ukuze wenze lokhu, sebenzisa i-immunoglobulin engena-intravenous, kanye ne-aspirin, okusiza ukunciphisa ukushisa. Ngezinye izikhathi, nge-Kawasaki syndrome, ukwelashwa kuhilela ukuphathwa kwe-corticosteroids (prednisolone). Lapho elulamekile, ingane izodinga ngezikhathi ezithile ukuthola i-ECG futhi ithathe i- aspirin , iphinde ibe ngaphansi kokuqondiswa okuqhubekayo kwe-cardiologist.