Yiziphi izizathu eziyinhloko zokuthuthukiswa kwama-APS?
Izimbangela zokuthuthukiswa kwe-antiphospholipid syndrome zimbalwa. Lezi zifo zingathuthuka ezimweni ezilandelayo:
- Uma owesifazane egula nge- systemic lupus erythematosus .
- Ubukhona ku-anamnesis we-thrombosis. Lapho izitsha ezihlanjululwayo ezinikezela igazi emathunjini, okuthiwa "izikhwama zesisu" ziqala, okubonakala ngokubonakala kokucindezela, ukucindezela okukhunjulwa endaweni yangasese emva kokungenisa.
- Ukunciphisa amaplatelets egazini, okungahambisani nezinkinga zokuphila.
- Ukutholakala komlando we-infarction ye-myocardial nezinye izifo ezihlobene nokukhathazeka kwe-cardiac circulatory.
I-antiphospholipid syndrome ibonakala kanjani?
Izimpawu ze-antiphospholipid syndrome, ngokuqondile kuxhomeke ezintweni eziningi. Ngakho kubaluleke kakhulu lezi zinto ezilandelayo:
- ubukhulu kanye nendawo yezitsha ezithintekile yi-pathology;
- inqubo yokuvala i-lumen kubo.
Ngakho-ke, esimweni lapho kuvinjelwa izitsha ezincane, ukwephulwa okuncane kakhulu kwemisebenzi yelungu elikudlayo kubonakala. Isibonelo, uma i-patency ye-vastic reticulums encane iphazanyiswa, kukhona ukwephulwa kwesivumelwano somzimba ngamunye we-myocardium, kepha uma ukukhanya kwe-lumen ye-coronary ishiyiwe, i-infarction ye-myocardial izokwenzeka.
Ngokuvamile i-antiphospholipid syndrome kwabesifazane abakhulelwe bangalingisa ezinye izifo ezihlukahlukene, ezibonakala izimpawu ezifanayo. Ngakho-ke, izibonakaliso ze-antiphospholipid syndrome zingabonakaliswa phambi kwe-lyvedo ebonakalayo (i-lacy, i-mesh mincane yemikhumbi esikhumbeni).
Ukwelashwa kwenziwa kanjani?
Ukwelashwa kwe-antiphospholipid syndrome ekukhulelweni kwenziwa ngaphansi kokulawulwa odokotela ababili: isazi sokubeletha kanye nesifo se-rheumatologist. Ukwelashwa okuyisisekelo kwalesi sifo kuwukusetshenziswa kwe-glucocorticoids ne-cytostatics. Ngokuqukethwe okuphezulu kwama-antibodies egazini, isisombululo kuphela ukuqhuba i-plasmapheresis (ukuhlanzwa kwegazi).