Antiphospholipid syndrome nokukhulelwa

I-Antiphospholipid syndrome (APS) iqoqo lezinkinga ezizimele ezibonakala ngokubunjwa kwenani elikhulu lama-antibodies kuma-phospholipids ekhona e-plasma yegazi (antiphospholipid antibodies). Phakathi kwabesifazane abahlukunyezwa ngokoqobo , isifo se-antiphospholipid syndrome sikhulu, futhi singama-28-43%. Ukucindezeleka okuyinhloko kwalesi sifo kuyi-thrombosis.

Yiziphi izizathu eziyinhloko zokuthuthukiswa kwama-APS?

Izimbangela zokuthuthukiswa kwe-antiphospholipid syndrome zimbalwa. Lezi zifo zingathuthuka ezimweni ezilandelayo:

  1. Uma owesifazane egula nge- systemic lupus erythematosus .
  2. Ubukhona ku-anamnesis we-thrombosis. Lapho izitsha ezihlanjululwayo ezinikezela igazi emathunjini, okuthiwa "izikhwama zesisu" ziqala, okubonakala ngokubonakala kokucindezela, ukucindezela okukhunjulwa endaweni yangasese emva kokungenisa.
  3. Ukunciphisa amaplatelets egazini, okungahambisani nezinkinga zokuphila.
  4. Ukutholakala komlando we-infarction ye-myocardial nezinye izifo ezihlobene nokukhathazeka kwe-cardiac circulatory.

I-antiphospholipid syndrome ibonakala kanjani?

Izimpawu ze-antiphospholipid syndrome, ngokuqondile kuxhomeke ezintweni eziningi. Ngakho kubaluleke kakhulu lezi zinto ezilandelayo:

Ngakho-ke, esimweni lapho kuvinjelwa izitsha ezincane, ukwephulwa okuncane kakhulu kwemisebenzi yelungu elikudlayo kubonakala. Isibonelo, uma i-patency ye-vastic reticulums encane iphazanyiswa, kukhona ukwephulwa kwesivumelwano somzimba ngamunye we-myocardium, kepha uma ukukhanya kwe-lumen ye-coronary ishiyiwe, i-infarction ye-myocardial izokwenzeka.

Ngokuvamile i-antiphospholipid syndrome kwabesifazane abakhulelwe bangalingisa ezinye izifo ezihlukahlukene, ezibonakala izimpawu ezifanayo. Ngakho-ke, izibonakaliso ze-antiphospholipid syndrome zingabonakaliswa phambi kwe-lyvedo ebonakalayo (i-lacy, i-mesh mincane yemikhumbi esikhumbeni). Futhi, izilonda ezingapheliyo zine-shin, ezinzima ukwelapha, futhi ngisho neziyaluyalu zomzimba, zingabonisa ukuba khona kwalesi sifo emzimbeni.

Ukwelashwa kwenziwa kanjani?

Ukwelashwa kwe-antiphospholipid syndrome ekukhulelweni kwenziwa ngaphansi kokulawulwa odokotela ababili: isazi sokubeletha kanye nesifo se-rheumatologist. Ukwelashwa okuyisisekelo kwalesi sifo kuwukusetshenziswa kwe-glucocorticoids ne-cytostatics. Ngokuqukethwe okuphezulu kwama-antibodies egazini, isisombululo kuphela ukuqhuba i-plasmapheresis (ukuhlanzwa kwegazi).